Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation)

Catalog No:
ATL-HPA055922-25
$401.00
Application: WB, ICC, IHC 
Clonality: Polyclonal 
Host: Rabbit 
Reactivity: Human 
Protein Description: melanoma inhibitory activity family, member 3
Gene Name: MIA3
Alternative Gene Name: FLJ39207, KIAA0268, TANGO, UNQ6077
Isotype: IgG
Interspecies mouse/rat: ENSMUSG00000038762: 25%, ENSRNOG00000058940: 26%
Entrez Gene ID: 375056
Uniprot ID: Q5JRA6
Buffer: 40% glycerol and PBS (pH 7.2). 0.02% sodium azide is added as preservative.
Storage Temperature: Store at +4°C for short term storage. Long time storage is recommended at -20°C.

Cognate Antibody/Antigen for Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation)
Antigen PrEST Antigen MIA3 (ATL-APrEST83592)
Documents & Links for Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation)
Datasheet Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation) Datasheet (External Link)
Vendor Page Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation) at Atlas

Documents & Links for Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation)
Datasheet Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation) Datasheet (External Link)
Vendor Page Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation)

Citations for Anti MIA3 pAb (ATL-HPA055922 w/enhanced validation) – 3 Found
Site-1 protease deficiency causes human skeletal dysplasia due to defective inter-organelle protein trafficking.
JCI Insight. 2018 Jul 26;3(14):e121596. doi: 10.1172/jci.insight.121596. eCollection 2018 Jul 26.  PubMed
Loss of TANGO1 Leads to Absence of Bone Mineralization.
JBMR Plus. 2021 Jan 13;5(3):e10451. doi: 10.1002/jbm4.10451. eCollection 2021 Mar.  PubMed
Collagen VII maintains proteostasis in dermal fibroblasts by scaffolding TANGO1 cargo.
Matrix Biol. 2022 Aug;111:226-244. doi: 10.1016/j.matbio.2022.06.008. Epub 2022 Jun 30.  PubMed